Incontinentia pigmenti, is a rare genodermatosis, also called Bloch-Sulzberger syndrome or Bloch-Siemens, that shows early at birth or in the neonatal period. In its classical form, the cutaneous symptomatology develops through three steps.
1st step, with evidence of injuries, of erythematic-vescicular-blistered kind and one wave after another, linearly positioned and involving upper body and limbs;haematic hypereosinophilia is also present.
2nd step, that pops up between the second and...